Juvenile Lichenoid Mycosis Fungoides: A Rare Variant Case Report with Clinical and Dermoscopic Features
Ouissal Essadeq *
Department of Dermatology-Venereology, Ibn Sina University Hospital, Mohammed V University, Rabat, Morocco.
Narjess Er-rachdy
Department of Dermatology-Venereology, Ibn Sina University Hospital, Mohammed V University, Rabat, Morocco.
Meriem Boubekri
Department of Anatomopathology, Ibn Sina University Hospital, Mohammed V University, Rabat, Morocco.
Taha Aaboudech
Department of Anatomopathology, Ibn Sina University Hospital, Mohammed V University, Rabat, Morocco.
Kaoutar Znati
Department of Anatomopathology, Ibn Sina University Hospital, Mohammed V University, Rabat, Morocco.
Laila Benzekri
Department of Dermatology-Venereology, Ibn Sina University Hospital, Mohammed V University, Rabat, Morocco.
Nadia Ismaili
Department of Dermatology-Venereology, Ibn Sina University Hospital, Mohammed V University, Rabat, Morocco.
*Author to whom correspondence should be addressed.
Abstract
Background: Lichenoid mycosis fungoides is an exceptionally rare entity in children, often posing significant diagnostic challenges due to its atypical presentation and resemblance to benign dermatoses.
Case Report: We report a pediatric case of lichenoid mycosis fungoides presenting with annular pigmented lesions and nail involvement. Dermoscopy raised initial suspicion, which was later confirmed only after repeated skin biopsies and immunohistochemical analysis. The diagnostic process illustrates the difficulty in confirming such rare variants and the need for persistence when clinical suspicion is high.
Importance: This case highlights a rare pediatric variant of mycosis fungoides and underscores the crucial role of dermoscopy and immunohistochemistry in its diagnosis. Given the limited literature on this condition in children, the report adds valuable insights for both dermatologists and pediatricians. It serves to raise awareness and may facilitate earlier recognition and appropriate management of similar atypical presentations in clinical practice.
Keywords: Lichenoid mycosis fungoides, pediatric, cutaneous T-cell lymphoma, dermoscopy